Description
Protein translocase and chaperone required for Complex III assembly; member of the AAA ATPase family; forms a homo-oligomeric complex in the mitochondrial inner membrane that translocates the C-terminal domain of Rip1p from the matrix across the inner membrane and delivers it to an assembly intermediate of respiratory Complex III; also required for assembly of the Qcr10p subunit; mutation is functionally complemented by human homolog BCS1L, linked to neonatal diseases [Source:SGD;Acc:S000002783]
Location
Chromosome IV: 1,225,166-1,226,536 reverse strand.
R64-1-1:BK006938.2
About this gene
This gene has 1 transcript (splice variant) and 197 orthologues.
Transcripts
